Nutritional deficiencies in dystrophic epidermolysis bullosa complicated by esophageal stricture in children: Exceptional association with Scurvy

Abstract

Epidermolysis bullosa (EB) is a set of rare, hereditary and chronic skin disorders, mainly affecting the skin and the pharyngo-oesophageal mucosa. Every patient with EB is different and his nutritional status can vary greatly depending on the type of EB and the extent of lesions. This case reports the nutritional complications of this disease, an exceptional association with Scurvy and the therapeutic challenges of esophageal stricture in these children.