An unusual case of primary ciliary dyskinesia associated with multiple drug intolerance syndrome

Authors

  • N Guirat Dhouib (1) Service de pédiatrie hôpital régional de Sidi Bouzid ; (2) Service régional de pharmacovigilance de Sfax, Tunisie ; (3) Service de pneumo-allergologie, CHU Hédi-Chaker de Sfax, Tunisie Author
  • H Ghozzi (1) Service de pédiatrie hôpital régional de Sidi Bouzid ; (2) Service régional de pharmacovigilance de Sfax, Tunisie ; (3) Service de pneumo-allergologie, CHU Hédi-Chaker de Sfax, Tunisie Author
  • N Bahloul (1) Service de pédiatrie hôpital régional de Sidi Bouzid ; (2) Service régional de pharmacovigilance de Sfax, Tunisie ; (3) Service de pneumo-allergologie, CHU Hédi-Chaker de Sfax, Tunisie Author
  • L Ben Mahmoud (1) Service de pédiatrie hôpital régional de Sidi Bouzid ; (2) Service régional de pharmacovigilance de Sfax, Tunisie ; (3) Service de pneumo-allergologie, CHU Hédi-Chaker de Sfax, Tunisie Author
  • Z Sahnoun (1) Service de pédiatrie hôpital régional de Sidi Bouzid ; (2) Service régional de pharmacovigilance de Sfax, Tunisie ; (3) Service de pneumo-allergologie, CHU Hédi-Chaker de Sfax, Tunisie Author
  • KH Zeghal (1) Service de pédiatrie hôpital régional de Sidi Bouzid ; (2) Service régional de pharmacovigilance de Sfax, Tunisie ; (3) Service de pneumo-allergologie, CHU Hédi-Chaker de Sfax, Tunisie Author

Keywords:

intolérance médicamenteuse multiple, enfant, dyskinésie ciliaire primitive

Abstract

The term multiple drug intolerance syndrome is used for patients who express adverse drug reactions to three or more drugs without a known immunological mechanism. It is a distinct clinical entity, different from cross-reactivity. The symptoms can range from a benign rash to life threatening syndromes like drug reaction with eosinophilia (DRESS) and systemic symptoms. We report a case of a child with primary ciliary dyskinesia who presented multiple drug intolerance syndrome.

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Published

2019-03-31