Bilateral papillary edema revealing aqueduct of Sylvius stenosis: about one case

Authors

  • R Bouraoui Service d'ophtalmologie B, Institut Hédi Rais, Boulevard 9 avril, 1006 Tunis, Tunisie Author
  • R Limaiem Service d'ophtalmologie B, Institut Hédi Rais, Boulevard 9 avril, 1006 Tunis, Tunisie Author
  • M Bouladi Service d'ophtalmologie B, Institut Hédi Rais, Boulevard 9 avril, 1006 Tunis, Tunisie Author
  • B Ben Romdhane Service d'ophtalmologie B, Institut Hédi Rais, Boulevard 9 avril, 1006 Tunis, Tunisie Author
  • F Mghaieth Service d'ophtalmologie B, Institut Hédi Rais, Boulevard 9 avril, 1006 Tunis, Tunisie Author
  • L El Matri Service d'ophtalmologie B, Institut Hédi Rais, Boulevard 9 avril, 1006 Tunis, Tunisie Author

Keywords:

œdème papillaire, sténose aqueduc de Sylvius, baisse de l'acuité visuelle

Abstract

Purpose: to report a case of a 13 year-old-girl who presented with symptomatic papilledema revealing hydrocephalus due to congenital aqueductal stenosis. Observation: A 13-year-old-girl with no significant medical history presented with progressive bilateral vision loss and headaches over the previous two months. The corrected visual acuity was 4/10. Fundus examination showed bilateral papilledema. Neuro-imaging revealed supra-tentoriel hydrocephalus due to congenital aqueductal stenosis. An endoscopic ventriculostomy was performed. Conclusion: Congenital aqueductal stenosis is a cause of non-communicating hydrocephalus. Its most common clinical manifestation is intracranial hypertension. MRI is considered the best diagnosis method.

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Published

2016-06-30

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Section

Case Report

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